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Pre-proof, online 12 January 2026
Routine blood biomarkers in patients with the PI*SZ genotype of alpha-1 antitrypsin deficiency: Data from the EARCO Registry
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Ane Lopez-Gonzaleza,#Robson Aparecido Prudentea,b,#Cristina Aljamaa,cCristina EsquinasdMaria Torres-DuraneAlice M TurnerfHanan TanashgCarlota Rodríguez-GarcíahAngelo Corsicoi,jEva BartošovskákCatarina GuimarãeslJosé Luis López-Camposm,nJens-Ulrik Stæhr Jenseno,pJosé María Hernández-PérezqChristian F. Clarenbachr,sKenneth R. ChapmantJuan Luis Rodríguez-HermosauMaria SucenavMarc Miravitllesa,c,n,
Corresponding author
marcm@separ.es

Corresponding author: Pneumology Department. Vall d’Hebron University Hospital, Pg. Vall d’Hebron 119-129, 08035 Barcelona, Spain
Miriam Barrechegurena,c,nthe EARCO group
a Department of Pneumology, Universitary Hospital Vall d´Hebron/ Vall d’Hebron Institut de Recerca (VHIR), Vall d’Hebron Barcelona Hospital Campus, CIBER de Enfermedades Respiratorias (CIBERES), Barcelona, Spain
b Clinical Hospital of the Faculty of Medicine of Botucatu, Botucatu, São Paulo, Brazil
c Department of Medicine, Universitat Autònoma de Barcelona, Bellaterra, Barcelona, 08193, Spain
d Faculty of Medicine and Health Sciences, University of Barcelona, Barcelona, Spain
e Pneumology Department, Hospital Álvaro Cunqueiro, NeumoVigo I+i Research Group, IIS Galicia Sur, Vigo, Spain / Centro de Investigación Biomédica en Red de Enfermedades Respiratorias (CIBERES). Instituto de Salud Carlos III, Madrid, Spain
f Respiratory Medicine, University Hospitals Birmingham NHS Foundation Trust, Birmingham, UK; School of Health Sciences, University of Birmingham, Birmingham, United Kingdom
g Department of Respiratory Medicine and Allergology, Skåne University Hospital, Lund University, Malmö, Sweden
h Pneumology Department, Complejo Hospitalario Clínico-Universitario de Santiago, Santiago de Compostela, Spain
i Pneumology Unit, IRCCS San Matteo Hospital Foundation, Pavia, Italy
j Department of Internal Medicine and Therapeutics, University of Pavia, Pavia, Italy
k Department of Pneumology, Thomayer Hospital, First Faculty of Medicine, Charles University, Prague, Czech Republic
l Pneumology Department, ULS Alto Ave, Guimarães, Portugal
m Unidad Médico-Quirúrgica de Enfermedades Respiratorias. Instituto de Biomedicina de Sevilla (IBiS). Hospital Universitario Virgen del Rocío, Universidad de Sevilla, Seville, Spain
n Centro de Investigación Biomédica en Red de Enfermedades Respiratorias (CIBERES). Instituto de Salud Carlos III, Madrid, Spain
o Section of Respiratory Medicine, Department of Medicine, Herlev and Gentofte Hospital, University of Copenhagen, Hellerup, Denmark
p Department of Clinical Medicine, Faculty of Health Sciences, University of Copenhagen, Denmark
q Pneumology Department, Hospital Universitario Nuestra Señora de La Candelaria, Santa Cruz de Tenerife, Spain
r Department of Pulmonology, University Hospital Zurich, Zurich, Switzerland
s Faculty of Medicine, University of Zurich, Zurich, Switzerland
t Asthma and Airway Center, University Health Network, Toronto Western Hospital, and Division of Respiratory Medicine, Department of Medicine, University of Toronto, Toronto, ON, Canada
u Pulmonology Department, Hospital Clínico San Carlos, Madrid, Spain
v Pulmonology Department, Unidade Local de Saúde de Santo António, Porto, Portugal
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Both authors contributed equally and must be considered first authors.

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