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Vol. 58. Issue 10.
Pages 713 (October 2022)
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Vol. 58. Issue 10.
Pages 713 (October 2022)
Clinical Image
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Multiple Cervicomediastinal Hamartomas Associated with Lymphangioleiomyomatosis
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Veysel Ayyildiza, Yener Aydinb,c,
Corresponding author
dryeneraydin@hotmail.com

Corresponding author.
, Hayri Ogulc,d
a Department of Radiology, Suleyman Demirel University, Medical Faculty, Isparta, Turkey
b Department of Thoracic Surgery, Ataturk University, Medical Faculty, Erzurum, Turkey
c Anesthesiology, Clinical Research Office, Ataturk University, Medical Faculty, Erzurum, Turkey
d Department of Radiology, Duzce University, Medical Faculty, Duzce, Turkey
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A 61-year-old female patient presented with a dyspnea for several years. She had a history of lymphangioleiomyomatosis and had undergone a right nephrectomy for angiomyolipoma. Multiple hamartomatous lesions were detected in the mediastinal and cervical regions on control thoracic computed tomography (Fig. 1).

Fig. 1.

Coronal chest CT scan (A) in mediastinal window demonstrates multiple parenchimal cystic lesions. Coronal chest (B) and neck (C) CT scans show multiple hamartomatous lesions (circle and arrows) with complex lipid density.

(0.12MB).

Angiomyolipoma is a tumoral lesion involving various combinations of smooth muscle, adipose tissue and vascular structures that most commonly affects the kidneys, but can also be observed in the liver, lung, lymph nodes, mediastinum, and retroperitoneal soft tissues. They are almost always benign neoplasms. However, they can cause massive or even fatal retroperitoneal hemorrhage. Lymphangioleiomyomatosis is a pathology that can diffusely affect the lungs and cause respiratory failure, spontaneous pneumothorax or chylothorax. There is the theory that lymphangioleiomyomatosis cells may actually arise from these angiomyolipomas.1,2 In these cases, resection for mediastinal and cervical angiomyolipomas can be considered, if possible.

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The authors received no financial support for the research and/or authorship of this article.

Conflict of interest

The authors declare that they have no conflict of interest to the publication of this article.

References
[1]
A. Cooper, L. Baugh, S. Kelley, H. Huang, J. Guileyardo.
Pulmonary lymphangioleiomyomatosis associated with aggressive renal angiomyolipoma.
Proc (Bayl Univ Med Cent), 31 (2018), pp. 81-83
[2]
S. Vaggers, P. Rice, B.K. Somani, R. Veeratterapillay, B.P. Rai.
Evidence-based protocol-led management of renal angiomyolipoma: a review of literature.
Turk J Urol, 47 (2021), pp. S9-S18
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