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Vol. 39. Issue 8.
Pages 370-372 (August 2003)
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Vol. 39. Issue 8.
Pages 370-372 (August 2003)
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Hipertensión pulmonar tromboembólica crónica asociada a fibrosis endomiocárdica del ventrículo derecho
Chronic thromboembolic pulmonary hypertension associated with endomyocardial fibrosis of the right ventricle
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E. Fernández Vázqueza,��
Corresponding author
efernandezv@hvn.sas.junta-andalucia.es

Correspondencia: Servicio de Neumología. Hospital Universitario Virgen de las Nieves. Avda. Fuerzas Armadas, s/n. 18014 Granada. España
, C. Lacárcel Bautistaa, B. Alcázar Navarretea, I. Casado Morenoa, A. Espejo Guerreroa, E. Ruiz Carazob
a Servicio de Neumología. Hospital Universitario Virgen de las Nieves. Granada. España
b Servicio de Radiodiagnóstico. Hospital Universitario Virgen de las Nieves. Granada. España
Article information

La hipertensión pulmonar tromboembólica crónica es una secuela infrecuente de la embolia pulmonar aguda no tratada o recurrente. Los mecanismos subyacentes para el fallo de resolución del trombo son todavía inciertos. La mayoría de los pacientes se diagnostican en un estadio tardío de la enfermedad, por lo que su historia natural no es completamente conocida

Presentamos el caso de una paciente de 51 años diagnosticada e intervenida de fibrosis endomiocárdica del ventrículo derecho que, tras varios años de evolución, desarrolló hipertensión pulmonar tromboembólica crónica

Palabras clave:
Fibrosis endomiocárdica
Hipertensión pulmonar tromboembólica crónica
Miocardiopatía restrictiva

Chronic thromboembolic pulmonary hypertension is a rare sequela to an acute untreated or recurrent pulmonary embolism. The mechanisms that underlie the failure to resolve the thrombus are still uncertain. As most patients are not diagnosed until a relatively late stage, little is known about the course of their illness

We report the case of a 51-year-old woman who had previously been diagnosed with and operated on for endomyocardial fibrosis of the right ventricle and who developed chronic thromboembolic pulmonary hypertension several years later

Key words:
Endomyocardial fibrosis
Chronic thromboembolic pulmonary hypertension
Restrictive cardiomyopathy
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Copyright © 2003. Sociedad Española de Neumología y Cirugía Torácica
Archivos de Bronconeumología

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