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Vol. 28. Issue 3.
Pages 119-121 (April 1992)
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Vol. 28. Issue 3.
Pages 119-121 (April 1992)
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Fibrosis pulmonar idiopátíca de rápida evolución. Síndrome de Hamman-Rich
Rapidly evolving idiopathic pulmonary fibrosis: Hamman-Rich syndrome
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V. Estrada Pérez, S. González Quijada, F. Del Río Gallegos, L. Audibert Mena, R.V. Estrada Saiz
Servicios de Medicina Interna 3, Hospital Universitario de San Carlos. Madrid
L. Ortega Medina*
* Anatomía Patológica. Hospital Universitario de San Carlos. Madrid
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Se presentan dos casos de fibrosis pulmonar idiopática de rápida evolución, conduciendo ambos al fallecimiento por insuficiencia respiratoria aguda, en un plazo inferior a los 60 días, sin respuesta al tratamiento con esferoides. En uno de los pacientes, los hallazgos anatomopatológicos eran sugestivos de neumonía intersticial descamativa y en el otro caso se apreciaba intensa fibrosis con áreas de panalización. El curso clínico coincide con la descripción inicial de fibrosis pulmonar idiopática por parte de Hamman y Rich.

We report two patients with rapidly evolving idiopathic pulmonary fibrosis who died because acute respiratory failure lasting less than 60 days which did not respond to steroid therapy. One patient presented pathologic findings suggestive of desquamative interstitial pneumonia and the other patient showed marked fibrosis. The clinical course coincides with the initial description of idiopathic pulmonary fibrosis by Hamman and Rich.

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Copyright © 1992. Sociedad Española de Neumología y Cirugía Torácica
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