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Vol. 43. Issue 7.
Pages 418-420 (January 2007)
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Vol. 43. Issue 7.
Pages 418-420 (January 2007)
Case Report
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Pulmonary Sclerosing Hemangioma in a Patient With Cowden Syndrome
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Félix Guerra-Gutiérreza,
Corresponding author
flaguers@hotmail.com

Correspondence: Dr. F.J. Álvarez-Gutiérrez. Servicio de Radiología. Hospital Universitario La Paz. Pº. de la Castellana, 261. 28046 Madrid. España
, Isabel Torres Sáncheza, Guillermo Gallardo-Madueñoa, Adrián Mariño-Enríquezb, Manuel Nistralb
a Servicio de Radiodiagnóstico, Hospital Universitario La Paz, Madrid, Spain
b Servicio de Anatomía Patológica, Hospital Universitario La Paz, Madrid, Spain
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Arch Bronconeumol. 2007;43:64110.1016/S1579-2129(07)60147-5
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We describe the case of an 18-year-old female with Cowden syndrome in whom a simple x-ray detected a solitary pulmonary nodule that was identified as a sclerosing hemangioma. Pulmonary sclerosing hemangioma is an unusual lung neoplasm which typically presents as a solitary peripheral nodule in asymptomatic women. Although the histology of this entity is well defined, its origin and treatment is debated. One of the main diagnostic problems is to histologically differentiate a pulmonary sclerosing hemangioma from a papillary lung carcinoma.

Key words:
Sclerosing hemangioma
Lung tumor
Cowden syndrome

Describimos el caso de una paciente de 18 años con síndrome de Cowden, en quien una radiografía simple objetivó un nódulo pulmonar solitario que resultó ser un hemangioma esclerosante. El hemangioma esclerosante de pulmón es una neoplasia pulmonar poco frecuente, que suele presentarse como un nódulo solitario periférico en mujeres asintomáticas. En la actualidad, aunque la histología del hemangioma esclerosante está bien definida, son objeto de discusión la histiogénesis de esta entidad y su tratamiento. Uno de los principales problemas diagnósticos es diferenciar histológicamente el hemangioma esclerosante del adenocarcinoma pulmonar con patrón papilar.

Palabras clave:
Hemangioma esclerosante
Tumores de pulmón
Síndrome de Cowden
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Copyright © 2007. Sociedad Española de Neumología y Cirugía Torácica (SEPAR)
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