Journal Information
Vol. 38. Issue 8.
Pages 399-400 (August 2002)
Share
Share
Download PDF
More article options
Vol. 38. Issue 8.
Pages 399-400 (August 2002)
Full text access
Osificación pulmonar dendriforme asociada con fibrosis pulmonar idiopática
Dendriform pulmonary ossification associated with idiopathic pulmonary fibrosis
Visits
11476
O. Trejo, A. Xaubet
Corresponding author
axaubet@clinic.ub.es

Correspondencia: Servei de Pneumologia. Hospital Clínic.Villarroel, 170. 08036 Barcelona
, A. Marin-Arguedas, A. Torres
Servei de Pneumologia. Institut Clínic de Pneumologia i Cirurgia Toràcica.Hospital Clínic. Idibaps. Universitat de Barcelona
J. Ramíreza, P. Luburichb
a Servei de Anatomia Patològica. Hospital Clínic. Idibaps. Universitat de Barcelona
b Servei de Radiodiagnòstic. Hospital Clínic. Idibaps. Universitat de Barcelona
This item has received
Article information
Abstract
Bibliography
Download PDF
Statistics

La osificación pulmonar difusa es una entidad poco frecuente en la que se produce una metaplasia ósea del pulmón y que suele asociarse con enfermedades que ocasionan lesiones pulmonares difusas. Existen dos tipos de osificación pulmonar: la dendriforme y la nodular. La forma dendriforme es la menos frecuente y se caracteriza por ramificaciones de estructura ósea a lo largo de las vías aéreas distales con islotes ocasionales de médula ósea. Se presenta un caso de osificación pulmonar difusa de tipo dendriforme asociada con fibrosis pulmonar idiopática. El diagnóstico se estableció mediante el examen histológico, que demostró la presencia de múltiples nódulos y espículas óseas ramificadas en la periferia del pulmón, principalmente en los lóbulos pulmonares inferiores, donde las lesiones fibróticas eran más evidentes

Palabras clave:
Fibrosis pulmonar idiopática
Osificación pulmonar

Diffuse pulmonary ossification, a rare condition characterized by metaplastic ossification of the lung, is usually associated with diseases causing diffuse pulmonary lesions. Two types –dendriform and nodular– have been identified. In dendriform ossification, the less common type, osseous ramifications occur along the distal airways, with occasional islets of bone marrow. We report a case of diffuse dendriform pulmonary ossification associated with idiopathic pulmonary fibrosis. The diagnosis was based on histological examination, which demonstrated multiple nodules and ramified osseous spicules around the lung, mainly at the lower lobes, where the fibrotic lesions were also most evident

Keywords:
Idiopathic pulmonary fibrosis
Pulmonary ossifica-tion
Full text is only aviable in PDF
Bibliografía
[1.]
D. Ethan, M.D. Fried, A. Thomas.
Extensive diffuse pulmonary ossification.
Chest, 102 (1992), pp. 1614-1615
[2.]
B. Felson, J. Schwarz, R. Lukin, H. Hawkins.
Idiopathic pulmonary ossification.
Radiology, 153 (1984), pp. 303-310
[3.]
P.A. Gevevois, M. Abehsera, C. Knoop, D. Jacobovitz, M. Estenne.
Disseminated pulmonary ossification in end-stage pulmonary fibrosis: CT demonstration.
Ajr, 162 (1994), pp. 1303-1304
[4.]
H. Luschka.
Verastige knochenbildung im parenchyma der lung.
Virchows Arch, 10 (1856), pp. 500-505
[5.]
J. Mendeloff.
Disseminated nodular pulmonary ossification in the Hamman-rich lung.
Am Rev Respir Dis, 103 (1971), pp. 269-274
[6.]
T. Ishida, K. Hosokawa, M. Munakata.
Extensive diffuse pulmonary ossification associated with idiopathic pulmonary fibrosis: thoracoscopic and computed tomographic findings.
J Bronchol, 4 (1997), pp. 225-228
[7.]
A.L.A. Katzenstein, J.L. Myers.
Idiopathic pulmonary fibrosis. Clinical relevance of pathologic classification.
Am J Resp Crit Care Med, 157 (1998), pp. 1301-1315
[8.]
K. Brown, D.F. Mund, D. Aberle, P. Batra, D.A. Young.
Intrathoracic calcifications: radiographic features and differential diagnosis.
Radiographics, 14 (1994), pp. 1247-1261
[9.]
R.W. Joines, V.L. Roggli.
Dendriform pulmonary ossification.
Arch Intern Med, 137 (1977), pp. 523-525
[10.]
N. Khalil, R.N. O'Connor, H.W. Unruh, P.W. Warren, K.C. Flanders, A. Kemp, et al.
Increased production and immunohistochemical localization of transforming growth factor-β in idiophtic pulmonary fibrosis.
Am J Resp Cell Mol Biol, 5 (1991), pp. 155-162
[11.]
R. Raghow.
Role of transforming growth factor-beta in repair and fibrosis.
Chest, 99 (1991), pp. S61-S65
[12.]
J.M. Jaderborg, R.F. Dunton.
Rare clinical diagnosis of dendriform pulmonary ossification.
Ann Thorac Surg, 71 (2001), pp. 2009-2011
Copyright © 2002. Sociedad Española de Neumología y Cirugía Torácica
Archivos de Bronconeumología
Article options
Tools

Are you a health professional able to prescribe or dispense drugs?